【DOI】10.3969/j.issn.1671 ̄6450.2023.08.017综述IgG4相关性疾病:警钟需长鸣胡豪综述何妙侠审校基金项目:上海市科委科技支撑项目(18411963000)作者单位:200433上海ꎬ海军军医大学长海医院病理科通信作者:何妙侠ꎬE ̄mail:hmm26@163.com【摘要】IgG4相关性疾病累及脏器众多ꎬ涉及范围广泛ꎬ临床表现多样ꎬ就诊科室繁杂ꎬ误诊率与漏诊率均较高ꎬ给诊断与鉴别诊断带来极大困难ꎮ文章通过对IgG4相关性疾病不同器官病变的特征、诊断标准以及鉴别诊断等进行分析总结ꎬ以期帮助临床及病理医生全面熟悉和掌握IgG4相关性疾病的特点ꎬ提高诊断警觉性和正确性ꎬ减少误诊率和漏诊率ꎮ【关键词】IgG4相关性疾病ꎻ临床特征ꎻ诊断ꎻ鉴别诊断【中图分类号】R593.2【文献标识码】AIgG4relateddiseases:alarmbellsneedtoringforalongtimeHuHaoꎬHeMiaoxia.DepartmentofPathologyꎬChang ̄haiHospitalꎬNavalMilitaryMedicalUniversityꎬShanghai200433ꎬChinaCorrespondingauthor:HeMiaoxiaꎬE ̄mail:hmm26@163.comFundingprogram:ScienceandTechnologySupportProjectofShanghaiScienceandTechnologyCommission(18411963000)【Abstract】IgG4relateddiseasesinvolvenumerousorgans,involveawiderangeofclinicalmanifestations,andhavecomplexmedicaldepartments.Themisdiagnosisandmisseddiagnosisratesarebothhigh,posinggreatdifficultiesfordiag ̄nosisanddifferentialdiagnosis.Thearticleanalyzesandsummarizesthecharacteristics,diagnosticcriteria,anddifferentialdiagnosisofdifferentorganlesionsinIgG4relateddiseases,inordertohelpclinicalandpathologicaldoctorsfullyunder ̄standandmasterthecharacteristicsofIgG4relateddiseases,improvediagnosticalertnessandaccuracy,andreducemisdi ̄agnosisandmisseddiagnosisrates.【Keywords】IgG4 ̄relateddiseases;Clinicalfeatures;Diagnosis;DifferentialdiagnosisIg...