25/1/19先天性巨结肠先天性巨结肠CongenitalmegacolonCongenitalmegacolon定义定义DefinationDefination•由于直肠或者结肠远端的肠管持续痉挛，粪便淤积在近端结肠，使该肠管肥厚、扩张•Rectalorcolonicintestinalhaspersistentspasmandfecaldepositionintheproximalcolonresultsinhypertrophyanddilatationinproximalsegment.Hirschsprung’sDisease,HD赫什朋氏病Aganglionosis先天性无神经节细胞症Hirschsprung’sDisease,HD赫什朋氏病Aganglionosis先天性无神经节细胞症英文名称Englishname概述概述SummarySummary•一种常见的消化道畸形•Acommondigestivetractmalformation•有遗传倾向，约1.4-7.8%•Geneticpredisposition,about1.4-7.8%•发病率为1:2000-5000•Incidencerateof1:2000-5000•男:女=4:1•M...
